2024 Tus sau: Elizabeth Oswald | [email protected]. Kawg hloov kho: 2024-01-13 00:07
Epidermolysis bullosa tau pom thawj zaug hauv lig 1800s. Nws yog ib tug tswv cuab ntawm tsev neeg ntawm cov kab mob hu ua blistering disease.
Puas yog dystrophic epidermolysis bullosa ib yam kab mob tsawg?
Epidermolysis bullosa acquisita (ib daim ntawv tau txais ntawm EB) yog ib yam tsis tshua muaj autoimmune tsis meej thiab tsis tau txais txiaj ntsig.
Ntau npaum li cas yog dystrophic epidermolysis bullosa?
Xav txog ua ke, qhov ntau ntawm kev rov ua dua thiab tseem ceeb dystrophic epidermolysis bullosa yog kwv yees li 3.3 ib lab tus tib neeg.
Tus neeg laus tshaj EB npaum li cas?
EB mob hnyav heev, mob hnyav thiab ntau zaus ua rau tuag taus ua ntej hnub nyoog 30. Dean Clifford yog ib tug ntawm cov menyuam yaus no. Tam sim no 39 xyoo, Dean tau kov yeej ntau yam kev nyuaj thiab tej zaum yog tus neeg laus tshaj plaws uas muaj tus kab mob hnyav dua.
Tus kab mob ntawm daim tawv nqaij Garrett Spaulding raug mob dab tsi?
Spaulding, ib tug tub hluas hnub nyoog 17 xyoo los ntawm Gustine, yug los nrog recessive dystrophic epidermolysis bullosa, los yog EB, ib qho kab mob tsawg uas ua rau pob khaus thiab kua muag ntawm daim tawv nqaij, tsim tej qhov txhab mob. EB npog txog 80 feem pua ntawm Spaulding lub cev, thiab vim muaj teeb meem thiab cov hlab ntsha puas, nws tsis tuaj yeem taug kev.
Pom zoo:
Leej twg pom dystrophic epidermolysis bullosa?
Nyob rau xyoo 1980s, Robert Burgeson, PhD, thiab nws pab pawg tshawb fawb ntawm Shriner's Tsev Kho Mob hauv Portland, Oregon, nrhiav pom hom-7 collagen thiab pab qhia tias cov neeg mob uas muaj dystrophic recessive. EB tsis muaj cov protein no.
Muaj pes tsawg hom epidermolysis bullosa muaj?
Epidermolysis bullosa (EB) yog ib hom kab mob ntawm daim tawv nqaij uas tshwm sim hauv kev kho mob los ntawm hlwv tsim los ntawm kev raug mob txhua yam. Muaj plaub hom tseem ceeb nrog rau lwm hom sub- txheeb xyuas. Muaj ib qho spectrum ntawm qhov hnyav, thiab nyob rau hauv txhua hom, ib tug tej zaum yuav mob me me los yog hnyav.
Thaum twg tau pom muaj kab mob epidermolysis?
Epidermolysis bullosa tau pom thawj zaug hauv lig 1800s. Nws yog ib tug tswv cuab ntawm tsev neeg ntawm cov kab mob hu ua blistering kab mob. EB tshwm sim hauv peb hom: simplex, junctional thiab dystrophic. Tus kab mob ntawm daim tawv nqaij Garrett Spaulding raug mob dab tsi?
Dab tsi yog dystrophic epidermolysis bullosa?
Dystrophic epidermolysis bullosa yog ib qho ntawm cov ntaub ntawv loj ntawm ib pawg neeg mob hu ua epidermolysis bullosa. Epidermolysis bullosa ua rau daim tawv nqaij ua kom tawg yooj yim thiab blister yooj yim. Cov hlwv thiab daim tawv nqaij yaig ua rau teb rau kev raug mob me me lossis kev sib txhuam, xws li txhuam lossis khawb.
Puas nrhiav tau lossis nrhiav tau?
Yog li, koj yuav tsum tau siv "could find". Lub modal verb, tau yog twb nyob rau hauv nws paste-form: ua. Yog li koj tsis tas yuav hloov pauv los nrhiav. Yuav nrhiav tau lossis nrhiav tau? "Ntaus" yog sib npaug. "