2024 Tus sau: Elizabeth Oswald | [email protected]. Kawg hloov kho: 2024-01-13 00:07
Nyob rau xyoo 1980s, Robert Burgeson, PhD, thiab nws pab pawg tshawb fawb ntawm Shriner's Tsev Kho Mob hauv Portland, Oregon, nrhiav pom hom-7 collagen thiab pab qhia tias cov neeg mob uas muaj dystrophic recessive. EB tsis muaj cov protein no.
Epidermolysis bullosa tuaj qhov twg?
Epidermolysis bullosa feem ntau yog los ntawm kev xeeb tub. Cov noob kab mob yuav kis tau los ntawm ib tus niam txiv uas muaj tus kab mob (autosomal dominant qub txeeg qub teg). Los yog nws yuav kis tau los ntawm ob leeg niam txiv (autosomal recessive qub txeeg qub teg) los yog tshwm sim raws li kev hloov pauv tshiab hauv tus neeg cuam tshuam uas tuaj yeem kis tau.
Dystrophic epidermolysis bullosa yog dab tsi?
Dystrophic epidermolysis bullosa yog ib qho ntawm cov ntaub ntawv loj ntawm ib pab pawg ntawm cov xwm txheej hu ua epidermolysis bullosa. Epidermolysis bullosa ua rau daim tawv nqaij tsis yooj yim heev thiab blister yooj yim. Cov hlwv thiab daim tawv nqaij yaig ua rau teb rau kev raug mob me me lossis kev sib txhuam, xws li txhuam lossis khawb.
Marky jaquez yog leej twg?
(KSNW) - Nees nkaum-xyoo-laus Marky Jaquez yug los nrog cov kab mob tsis tshua muaj tawv nqaij "Epidermolysis bullosa," tseem hu ua butterfly syndrome. Nws niam, Melissa Jaquez, uas khiav nws tus account TikTok, hais tias cov yeeb yaj kiab ntawm nws tus tub raug chij thiab muab tso tseg los ntawm TikTok.
Puas yog dystrophic epidermolysis bullosa ib yam kab mob tsawg?
Epidermolysis bullosa acquisita (ib daim ntawv tau txais ntawm EB) yog tsis tshua muajautoimmune disorder thiab tsis tau txais txiaj ntsig.
Pom zoo:
Thaum twg dystrophic epidermolysis bullosa nrhiav tau?
Epidermolysis bullosa tau pom thawj zaug hauv lig 1800s. Nws yog ib tug tswv cuab ntawm tsev neeg ntawm cov kab mob hu ua blistering disease. Puas yog dystrophic epidermolysis bullosa ib yam kab mob tsawg? Epidermolysis bullosa acquisita (ib daim ntawv tau txais ntawm EB) yog ib yam tsis tshua muaj autoimmune tsis meej thiab tsis tau txais txiaj ntsig.
Muaj pes tsawg hom epidermolysis bullosa muaj?
Epidermolysis bullosa (EB) yog ib hom kab mob ntawm daim tawv nqaij uas tshwm sim hauv kev kho mob los ntawm hlwv tsim los ntawm kev raug mob txhua yam. Muaj plaub hom tseem ceeb nrog rau lwm hom sub- txheeb xyuas. Muaj ib qho spectrum ntawm qhov hnyav, thiab nyob rau hauv txhua hom, ib tug tej zaum yuav mob me me los yog hnyav.
Thaum twg tau pom muaj kab mob epidermolysis?
Epidermolysis bullosa tau pom thawj zaug hauv lig 1800s. Nws yog ib tug tswv cuab ntawm tsev neeg ntawm cov kab mob hu ua blistering kab mob. EB tshwm sim hauv peb hom: simplex, junctional thiab dystrophic. Tus kab mob ntawm daim tawv nqaij Garrett Spaulding raug mob dab tsi?
Dab tsi yog dystrophic epidermolysis bullosa?
Dystrophic epidermolysis bullosa yog ib qho ntawm cov ntaub ntawv loj ntawm ib pawg neeg mob hu ua epidermolysis bullosa. Epidermolysis bullosa ua rau daim tawv nqaij ua kom tawg yooj yim thiab blister yooj yim. Cov hlwv thiab daim tawv nqaij yaig ua rau teb rau kev raug mob me me lossis kev sib txhuam, xws li txhuam lossis khawb.
Koj puas pom leej twg pom koj cov nkoj?
Fleet sau tuaj yeem pom leej twg saib lawv cov Fleets, suav nrog cov nyiaj uas muaj kev tiv thaiv Tweets, los ntawm nias rau hauv lawv cov Fleets thiab coj mus rhaub rau ' Pom Los Ntawm' cov ntawv hauv qab. Koj puas pom leej twg saib koj cov nkoj?