2024 Tus sau: Elizabeth Oswald | [email protected]. Kawg hloov kho: 2024-01-13 00:07
Epidermolysis bullosa (EB) yog ib hom kab mob ntawm daim tawv nqaij uas tshwm sim hauv kev kho mob los ntawm hlwv tsim los ntawm kev raug mob txhua yam. Muaj plaub hom tseem ceeb nrog rau lwm hom sub- txheeb xyuas. Muaj ib qho spectrum ntawm qhov hnyav, thiab nyob rau hauv txhua hom, ib tug tej zaum yuav mob me me los yog hnyav.
Puas muaj ntau hom epidermolysis bullosa?
epidermolysis bullosa simplex (EBS) - hom ntau tshaj plaws, uas tuaj yeem muaj xws li mob me me, uas tsis tshua muaj kev pheej hmoo ntawm cov teeb meem loj, mus rau qhov hnyav. dystrophic epidermolysis bullosa (DEB) - uas tuaj yeem sib txawv ntawm me me mus rau qhov hnyav. junctional epidermolysis bullosa (JEB) - ib daim ntawv tsis tshua muaj EB uas txawv ntawm nruab nrab mus rau hnyav.
Muaj pes tsawg tus neeg mob epidermolysis bullosa muaj?
Qhov tseeb ntawm cov kab mob epidermolysis bullosa simplex tsis paub, tab sis tus mob no kwv yees yuav cuam tshuam 1 ntawm 30,000 txog 50,000 tus neeg. Hom kab mob hauv zos yog hom kab mob ntau tshaj plaws.
4 subdivisions ntawm EB yog dab tsi?
EB muaj plaub hom loj raws li qhov chaw ntawm cov kab mob hlwv hauv cov txheej txheem ntawm daim tawv nqaij: epidermolysis bullosa simplex (EBS), junctional EB (JEB), dystrophic EB (DEB), thiab Kindler syndrome.
Qhov twg yog epidermolysis bullosa feem ntau?
Cov hom tseem ceeb ntawm epidermolysis bullosa yog: Epidermolysis bullosa simplex. Qhov no yog daim ntawv tshaj plaws. Nws tsim nyob rau hauv txheej txheej ntawm daim tawv nqaij thiab feem ntau cuam tshuam rau xib teg thiab ko taw.
Pom zoo:
Thaum twg dystrophic epidermolysis bullosa nrhiav tau?
Epidermolysis bullosa tau pom thawj zaug hauv lig 1800s. Nws yog ib tug tswv cuab ntawm tsev neeg ntawm cov kab mob hu ua blistering disease. Puas yog dystrophic epidermolysis bullosa ib yam kab mob tsawg? Epidermolysis bullosa acquisita (ib daim ntawv tau txais ntawm EB) yog ib yam tsis tshua muaj autoimmune tsis meej thiab tsis tau txais txiaj ntsig.
Leej twg pom dystrophic epidermolysis bullosa?
Nyob rau xyoo 1980s, Robert Burgeson, PhD, thiab nws pab pawg tshawb fawb ntawm Shriner's Tsev Kho Mob hauv Portland, Oregon, nrhiav pom hom-7 collagen thiab pab qhia tias cov neeg mob uas muaj dystrophic recessive. EB tsis muaj cov protein no.
Muaj pes tsawg hom nyiaj muaj?
Zoo, raws li koj tau twv los ntawm lub npe, muaj 180 cov nyiaj tam sim no thoob plaws ntiaj teb, raws li tau lees paub los ntawm United Nations. Yuav ua li cas hom nyiaj muaj? Tus Swiss franc, Canadian duas, Australian thiab New Zealand duas, thiab South African rand ncig tawm cov npe ntawm cov txiaj ntsig zoo tshaj plaws U.
Dab tsi yog dystrophic epidermolysis bullosa?
Dystrophic epidermolysis bullosa yog ib qho ntawm cov ntaub ntawv loj ntawm ib pawg neeg mob hu ua epidermolysis bullosa. Epidermolysis bullosa ua rau daim tawv nqaij ua kom tawg yooj yim thiab blister yooj yim. Cov hlwv thiab daim tawv nqaij yaig ua rau teb rau kev raug mob me me lossis kev sib txhuam, xws li txhuam lossis khawb.
Muaj pes tsawg hom tsis pom muaj?
Tshaj tawm tias tseem muaj tshaj tsib lab hom tos kom pom. pes tsawg hom tsiaj tsis pom? - Muaj kwv yees li 8.7 lab cov nroj tsuag thiab tsiaj nyob hauv peb lub ntiaj teb. Qhov no txhais tau hais txog 86 feem pua ntawm hom av thiab 91 feem pua ntawm cov tsiaj hiav txwv tseem tsis tau tshawb pom.