Agammaglobulinemia yog ib pawg pawg ntawm cov tshuaj tiv thaiv kab mob tsis zootus yam ntxwv los ntawm cov tshuaj tiv thaiv qis hauv cov ntshav vim tsis muaj cov lymphocytes tshwj xeeb hauv cov ntshav thiab cov qog ntshav. Cov tshuaj tiv thaiv yog cov proteins (immunoglobulins, (IgM), (IgG) thiab lwm yam) uas yog qhov tseem ceeb thiab cov khoom tseem ceeb ntawm lub cev tiv thaiv kab mob.
Puas agammaglobulinemia ua rau tuag taus?
B hlwb yog ib feem ntawm lub cev tiv thaiv kab mob thiab feem ntau tsim cov tshuaj tiv thaiv kab mob (tseem hu ua immunoglobulins), uas tiv thaiv lub cev los ntawm kev kis kab mob los ntawm kev txhawb nqa kev tiv thaiv kab mob. Cov neeg mob uas tsis kho XLA yog qhov ua rau muaj kab mob hnyav thiab tuag taus.
agammaglobulinemia kis tau li cas?
Txawm li cas los xij, cov neeg mob agammaglobulinemia tuaj yeem muab qee yam ntawm tshuaj tiv thaiv kab mob uas lawv tsis muaj. Cov tshuaj tiv thaiv tau muab rau hauv daim ntawv ntawm immunoglobulins (lossis gamma globulins) thiab tuaj yeem muab ncaj qha rau hauv cov hlab ntshav (intravenously) lossis hauv qab ntawm daim tawv nqaij (subcutaneously).
Leej twg pom agammaglobulinemia?
Nyob rau xyoo 1952, Ogden Bruton, tus kws kho mob menyuam yaus ntawm W alter Reed Army Tsev Kho Mob hauv Washington, DC (Daim duab 1), tau tshaj tawm thawj kis ntawm agammaglobulinemia hauv lub cev hauv 8 xyoo. - tus tub hluas uas raug kev mob pneumococcal sepsis.
XLA puas yog kab mob autoimmune?
Txawm hais tias cov neeg mob uas muaj XLA feem ntau yog xav tias muaj kev pheej hmoo tsawg ntawm autoimmune lossis inflammatory diseasepiv rau lwm yamPIDD pawg, cov ntaub ntawv los ntawm tus neeg mob daim ntawv ntsuam xyuas no thiab daim ntawv teev npe hauv lub tebchaws qhia tias feem ntau ntawm cov neeg mob XLA muaj cov tsos mob zoo ib yam nrog kev kuaj mob caj dab, …
