2024 Tus sau: Elizabeth Oswald | [email protected]. Kawg hloov kho: 2024-01-13 00:07
NON-NEPHROPATHIC CYSTINOSIS. Kuj hu ua ocular lossis "benign" cystinosis, daim ntawv no feem ntau cuam tshuam rau cov neeg laus thaum hnub nyoog nruab nrab; Nws yog ib zaug hu ua neeg laus cystinosis. Kab mob raum tsis tshwm sim hauv cov neeg no. Qhov teeb meem tshwm sim tsuas yog qhov muag xwb.
Neb nephropathic cystinosis yog dab tsi?
Nephropathic cystinosis yog ib yam kab mob tsis tshua muajuas feem ntau tshwm sim hauv cov me nyuam mos thiab cov me nyuam thaum yau. Nws yog ib qho mob mus ntev, tab sis muaj kev kho mob, xws li kev kho cysteamine thiab hloov lub raum, tau tso cai rau cov neeg muaj tus kab mob nyob ntev.
Tus kws kho mob twg kho nephropathic cystinosis?
A nephrologist yog tus kws kho mob tshwj xeeb hauv lub raum thiab yog thawj tus kws kho mob rau cov neeg mob cystinosis.
Cystinosis congenital yog dab tsi?
Cystinosis yog ib yam kab mob tsis tshua muaj caj ces uas ua rau muaj kev sib txuam ntawm cov amino acid cystine hauv cov hlwb, tsim cov pob zeb uas tuaj yeem tsim thiab ua rau cov hlwb puas. Cov crystals no tsis zoo rau ntau lub cev hauv lub cev, tshwj xeeb tshaj yog rau lub raum thiab qhov muag.
Puas cystinosis ua rau lub raum pob zeb?
Cov tsos mob tshwm sim feem ntau ntawm cov kab mob uas tsis yog nephropathic (ocular) cystinosis yog cov khoom siv lead ua nyob rau hauv lub pob muag ntawm lub qhov muag, uas ua rau mob thiab ua rau lub teeb pom kev zoo (photosensitivity). Cov neeg uas tsis yog nephropathic cystinosis feem ntau tsis tsim teeb meem raum lossis ib qho ntawmLwm cov tsos mob cuam tshuam nrog cystinosis.
Pom zoo:
Puas yog cov dab dab dab dab dab dab dab dab dab dab dab dab?
Myth: Ib tug dab tshos tsis yog neeg ncaj ncees yog tiasnws haum yog. Fact: Tu siab, qhov no yog ib lo lus tsis tseeb uas tau raug perpetuated los ntawm aversive trainers. Txawm hais tias haum rau lub caj dab kom zoo khawb rau hauv cov tawv nqaij rhiab nyob ib ncig ntawm lub caj dab, uas ua rau muaj kev puas tsuaj loj rau cov thyroid, esophagus, thiab trachea.
Dab tsi yog tus bestiary hauv dab dab dab?
Wiki Targeted (Kev Ua Si) Beasts yog cov lus hu uas muab Metropolitan Era monsters txhawb nqa rau stats nrog rau cov txiaj ntsig hauv kev sib ntaus sib tua. Tus Bestiary tuaj yeem kho tau ntawm qib 18, qhov twg cov neeg ua si tuaj yeem qhib thiab nce qib Beasts los txhim kho lawv lub zog thiab cov teebmeem.
Puas yog cystinosis autosomal dominant?
Cystinosis yog tshwm sim los ntawm kev hloov pauv ntawm CTNS gene thiab tau txais los ua ib qho autosomal recessive disease. cystinosis ua dab tsi rau lub cev? Nyob rau hauv cov neeg uas muaj cystinosis, ib qho kev tsim ntawm cystine tuaj yeem ua rau tsim cov muaju.
Dab tsi yog kev xav ntawm autonomists dab tsi yog qhov kev xav ntawm kev zoo nkauj ntawm kev coj ncaj ncees?
Kev lig kev cai, muaj ob txoj haujlwm tawm tsam kev xav txog kev coj ua raws li kev cai lij choj ntawm kev ntsuas kev ncaj ncees ntawm kev kos duab: 'kev coj ncaj ncees kev ncaj ncees Ethics lossis kev coj ncaj ncees yog ib ceg ntawm kev xav uas "
Puas yog cov dab dab dab dab dab dab tau them?
OHL cov neeg ua si tsis tau nyiaj hli, vim lawv tsis raug lees paub tias yog cov neeg ua haujlwm raws li Txoj Cai Kev Ua Haujlwm. Txawm li cas los xij, lawv suav nrog cov txiaj ntsig xws li nyiaj rov qab txhua xyoo, tag nrho cov nqi kawm ntawv them, thiab daim pib pub dawb.