Polyglandular deficiency syndromes (PDS) yog tus yam ntxwv los ntawm kev ua ntu zus lossis ib txhij tsis txaus hauv kev ua haujlwm ntawm ntau lub qog endocrine uas muaj qhov ua rau. Etiology feem ntau yog autoimmune. Categorization nyob ntawm kev sib xyaw ua ke ntawm qhov tsis zoo, uas poob hauv 1 ntawm 3 hom.
Dab tsi ua rau Polyglandular syndrome?
Nws xav tias tshwm sim los ntawm ib qho tsis txaus ntseeg hauv lub cev tiv thaiv kab mob. Qhov teeb meem no ua rau muaj cov thyroid secretion (hyperthyroidism), qhov loj ntawm cov thyroid caj pas thiab protrusion ntawm lub qhov muag. Tsis paub qhov tseeb ntawm qhov teeb meem no. Nws tau xav tias yuav tau txais txiaj ntsig raws li qhov autosomal recessive zoo.
YPolyglandular Syndrome yog dab tsi?
Autoimmune polyglandular syndrome type 1 (APS-1) yog ib qho tsis tshua muaj thiab tsis tshua muaj kev cuam tshuam los ntawm kev tiv thaiv kab mob hauv lub cev tsis ua haujlwm nrog ntau yam autoimmunities. Nws tshwm sim raws li ib pawg ntawm cov tsos mob suav nrog qhov muaj feem cuam tshuam txog lub neej ntawm cov qog endocrine thiab kev ua haujlwm ntawm plab hnyuv.
autoimmune Endocrinopathy yog dab tsi?
Autoimmune polyendocrine syndrome yog ib yam kab mob tsis tshua muaj tshwm sim uas lub cev tiv thaiv kab mob ua yuam kev tawm tsam ntau lub cev thiab cov khoom nruab nrog cev. Cov mucous daim nyias nyias thiab cov qog adrenal thiab cov qog parathyroid feem ntau cuam tshuam, txawm tias lwm cov ntaub so ntswg thiab cov kabmob tuaj yeem koom nrog.
Neeg dab tsi ua rau tib neeg autoimmunePolyglandular Syndrome?
Autoimmune polyglandular syndrome type 1 yog tus cwj pwm los ntawm triad ntawm cov kab mob ntev mucocutaneous candidiasis, hypoparathyroidism, thiab adrenal insufficiency. Nws yog vim kev hloov pauv hauv AIRE genethiab tau txais txiaj ntsig los ntawm autosomal recessive yam.
