2024 Tus sau: Elizabeth Oswald | [email protected]. Kawg hloov kho: 2024-01-13 00:07
Agammaglobulinemia (ARA) X-Txuas Agammaglobulinemia (XLA) tau piav qhia thawj zaug hauv 1952 los ntawm Dr. Ogden Bruton. Tus kab mob no, qee zaum hu ua Bruton's Agammaglobulinemia lossis Congenital Agammaglobulinemia, yog ib qho ntawm thawj cov kab mob tiv thaiv kab mob uas raug txheeb xyuas.
Qhov txawv ntawm Hypogammaglobulinemia thiab agammaglobulinemia yog dab tsi?
"Hypogammaglobulinemia" feem ntau yog txuam nrog "agammaglobulinemia". Thaum lub sij hawm tom kawg yog siv (raws li hauv "X-txuas agammaglobulinemia") nws txhais tau hais tias gamma globulins tsis yog txo qis, tab sis tsis ua tiav.
Dab tsi ua rau agammaglobulinemia?
X-linked agammaglobulinemia yog tshwm sim los ntawm kev hloov caj ces. Cov neeg mob tsis tuaj yeem tsim cov tshuaj tiv thaiv kab mob uas tiv thaiv kab mob. Kwv yees li 40% ntawm cov neeg mob muaj ib tsev neeg uas muaj.
Btk deficiency yog dab tsi?
Ib ob peb qhov kev hloov pauv hauv BTK noob tau pom tias ua rau muaj kev sib cais loj hlob hormone deficiency hom III, ib qho mob uas tshwm sim los ntawm kev loj hlob qeeb, luv luv, thiab lub cev tsis muaj zog. Kev hloov pauv uas ua rau tus mob no ua rau muaj qhov tsis ua haujlwm ntawm BTK protein.
XLA yog SCID?
XLA kuj yog keeb kwm yuam kev raws li Kev Tiv Thaiv Kab Mob hnyav(SCID), kev tiv thaiv kab mob hnyav dua ("Bubble tub"). Ib hom mobntawm lab nas, XID, yog siv los kawm XLA. Cov nas no muaj qhov hloov pauv ntawm tus nas Btk noob, thiab nthuav tawm qhov zoo sib xws, tsis tau mob me, tiv thaiv kab mob tsis muaj zog xws li hauv XLA.
Pom zoo:
Thaum twg dystrophic epidermolysis bullosa nrhiav tau?
Epidermolysis bullosa tau pom thawj zaug hauv lig 1800s. Nws yog ib tug tswv cuab ntawm tsev neeg ntawm cov kab mob hu ua blistering disease. Puas yog dystrophic epidermolysis bullosa ib yam kab mob tsawg? Epidermolysis bullosa acquisita (ib daim ntawv tau txais ntawm EB) yog ib yam tsis tshua muaj autoimmune tsis meej thiab tsis tau txais txiaj ntsig.
Thaum twg nrhiav tau dysarthria?
Early in 1969 , Darley et al. txhais tau tias dysarthria yog ib lo lus sib sau ua ke rau kev hais lus tsis zoo. Kev faib tawm ntawm dysarthria suav nrog flaccid dysarthria, spastic dysarthria, ataxic dysarthria, hypokinetic dysarthria, hyperkinetic hyperkinetic Hyperkinesia yog ib lub xeev ntawm kev ntxhov siab ntau dhauuas muaj ntau yam kab mob uas cuam tshuam rau lub peev xwm.
Thaum twg tarrytown nrhiav tau?
Ib lub zos nrog tob Dutch cov hauv paus hniav, Tarrytown tau teeb tsa los ntawm Europeans hauv 1640, thiab koom ua ke hauv 1870. Thaum pw tsaug zog Hollow nrhiav tau? Keeb Kwm Ib zaug ib feem ntawm cov cuab yeej cuab tam ntawm tus tub lag luam Frederick Philipse, nws tau koom ua North Tarrytown hauv 1874, plaub xyoos tom qab kev koom ua ke ntawm Tarrytown.
Thaum twg tau txais kev pom zoo nrhiav tau?
In 2009, peb tus tsim thiab CEO Steve Marshall tau txheeb xyuas lub sijhawm hauv kev lag luam pov hwm lub neej thiab Reassured tau tsim. Peb pab tsev neeg tiv thaiv qhov tseem ceeb tshaj plaws rau lawv; Peb Lub Hom Phiaj rau 2020 yog los tiv thaiv ntau dua 200,000 tsev neeg hauv tebchaws Askiv.
Puas nrhiav tau lossis nrhiav tau?
Yog li, koj yuav tsum tau siv "could find". Lub modal verb, tau yog twb nyob rau hauv nws paste-form: ua. Yog li koj tsis tas yuav hloov pauv los nrhiav. Yuav nrhiav tau lossis nrhiav tau? "Ntaus" yog sib npaug. "