2024 Tus sau: Elizabeth Oswald | [email protected]. Kawg hloov kho: 2024-01-13 00:07
Lub aetiology ntawm porphyria cutanea tarda (PCT) tsis tau qhia meej, tab sis qhov muaj peev xwm ntawm autoimmune mechanism tau raug npaj . Peb tshaj tawm ib rooj plaub ntawm kev kho mob tsis paub txog PCT nrog autoimmune hypothyroidism, alopecia universalis alopecia universalis Alopecia universalis (AU) yogmob tshwm sim los ntawm tag nrho cov plaub hau ntawm tawv taub hau thiab lub cev. Nws yog ib daim ntawv siab heev ntawm alopecia areata, ib qho mob uas ua rau ib puag ncig ntawm cov plaub hau poob. https://rarediseases.info.nih.gov › kab mob › alopecia-universalis
Alopecia universalis | Genetic and Rare Disease Information Center
thiab vitiligo nrog cov thyroid thiab parietal cell ncig cov tshuaj tiv thaiv.
kab mob porphyria yog dab tsi?
Porphyria (por-FEAR-e-uh) yog hais txog pab pawg ntawm cov kab mob uas tshwm sim los ntawm kev tsim cov tshuaj ntuj tsim tawm porphyrin hauv koj lub cev. Porphyrins yog qhov tseem ceeb rau kev ua haujlwm ntawm hemoglobin - cov protein hauv koj cov qe ntshav liab uas txuas rau porphyrin, khi hlau, thiab nqa oxygen rau koj lub cev thiab cov ntaub so ntswg.
Puas mob sib kis mob porphyria yog kab mob autoimmune?
Tus mob porphyria (AIP) tau txais txiaj ntsig li cas? AIP tau txais txiaj ntsig los ntawm autosomal dominant zam, uas txhais tau hais tias tsuas yog ib qho ntawm ob lub noob HMBS yuav tsum muaj cov kab mob ua rau hloov pauv kom txo qis kev ua haujlwm enzyme thiab ua rau cov tsos mob.
Lub neej expectancy yog dab tsintawm ib tug neeg nrog porphyria?
Cov neeg mob porphyria feem ntau muaj ib txwm muaj sia nyob. Txawm li cas los xij, cov neeg uas muaj kab mob siab porphyria yog qhov muaj feem pheej hmoo ntawm kev mob ntshav siab, kab mob raum ntev, thiab kab mob siab hepatocellular (mob qog noj ntshav), uas tuaj yeem txo lawv txoj sia.
Puas yog porphyria yog kab mob ntshav?
Porphyrias yog ib pawg ntawm cov ntshav tsis tshua muaj tshwm sim. Cov neeg uas muaj cov kab mob no muaj teeb meem ua cov khoom hu ua heme hauv lawv lub cev. Heme yog tsim los ntawm lub cev tshuaj hu ua porphyrin, uas yog khi rau hlau. Heme yog ib feem ntawm hemoglobin, protein nyob rau hauv cov qe ntshav liab uas nqa oxygen.
Pom zoo:
Puas yog kev ua xua yog kab mob autoimmune?
“Hauv autoimmunity, muaj ntau hom T-cell koom nrog kev ua xua. Hauv cov lus teb autoimmune, kev puas tsuaj tshwm sim. Nrog rau kev ua xua, lub cev tiv thaiv kab mob overreacts rau cov kab mob tsis haum. Qhov txaus siab, qhov no yog tib hom lus teb uas tshem tawm cov kab mob, kab mob, thiab kab mob ntawm lub cev.
Puas yog tus kab mob tseem yog kab mob autoimmune?
Tus neeg laus-pib tseem tus kab mob yog tus mob autoimmune. Qhov no txhais tau hais tias tus mob yog tshwm sim los ntawm koj lub cev tiv thaiv kab mob. Lub cev tiv thaiv kab mob tiv thaiv peb ntawm kev kis kab mob thiab lwm yam kev hem thawj rau lub cev, tab sis hauv AOSD nws ua rau koj lub cev ua yuam kev.
Cov kab kab kab kab kab ua kab mob txaus ntshai npaum li cas?
Nyob rau hauv peb thiab tom ntej instars ntawm lawv txoj kev loj hlob, Pine processionary caterpillars yog mob heev rau daim tawv nqaij ntawm tib neegthiab lwm yam tsiaj. Kev sib cuag yooj yim nrog cov plaub hau ntawm kab ntsig tuaj yeem ua rau pob khaus hnyav (urticaria) thiab khaus qhov muag, thiab qee tus neeg yuav muaj kev fab tshuaj.
Puas yog eosinophilic asthma yog tus kab mob autoimmune?
Thaum eosinophilic hawb pob yog ib lub cev tiv thaiv kab mob ntsig txog kev ua xua, ntau tus neeg kuaj pom nws tsis raug kev fab tshuaj xws li pwm, pwm, lossis lwm yam tsis haum. Puas yog eosinophilic asthma yog autoimmune? Eosinophils yog ib qho tseem ceeb ntawm kev mob hawb pob, hypereosinophilic syndromes, thiab eosinophilic plab hnyuv kab mob.
Puas yog menyuam yaus mob caj dab yog kab mob autoimmune?
Cov menyuam yaus mob caj dab yog tus kab mob autoimmune. Qhov ntawd txhais tau hais tias lub cev tiv thaiv kab mob, uas ib txwm tiv thaiv lub cev los ntawm cov khoom txawv teb chaws, tawm tsam lub cev. Tus kab mob no kuj yog idiopathic, uas txhais tau hais tias tsis muaj ib qho laj thawj tseeb.